Currently the child is doing well, walks with a limp and the calf is supple without palpable tumor.
Discussion: Congenital fibrosarcoma is a pediatric spindle-cell tumor of soft tissues that usually presents before the age of 2 years. Although these tumors display histological features of malignancy and frequently recur, they have a relatively good prognosis and only rarely metastasize. Soft tissues tumors account for 7% of the malignant tumors in childhood and fibro- and myoblastic tumors account for 12% of the soft tissues tumors in childhood.
A recent study about the follow-up of congenital fibrosarcoma at CHU NECKER – Enfants Malades (Paris) by Dr J-C FOURNET revealed these features of the mass:
Age : newborn to 2 years old with neonatal diagnosis in 80% of the cases.
Sex : M > F ( x 1,7)
Localization : Head and neck 19%, trunk 31%, abdomen and retroperitoneum 8%, limbs 42 %
Recurrence : 5-50%
Metastasis : 0-25%
Mortality rate : 23%
A prenatal diagnosis is impossible. Diagnosis can only be established by biopsy and t(12 ;15) (p13 ;q25 ) translocation when found, gives a better prognosis.